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Blue Cone Monochromacy

Disease ID: disease_node_19992

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DbxrefGARD:917, MIM:303700
SubclassofDOID_0080012, DOID_13911
Data SourceDOID
Doid Labelblue cone monochromacy
Doid DescriptionAn achromatopsia that is characterized by severely impaired color discrimination, low visual acuity, nystagmus, photophobia due to the absence of functional long wavelength-sensitive and medium wavelength-sensitive cones in the retina and has_material_basis_in alteration in the red (OPN1LW) and green (OPN1MW) visual pigment gene cluster on chromosome Xq28 or in the locus control region for the red and green pigment genes, located adjacent to and 5-prime of the pigment gene cluster. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_19992
Doid IdDOID_0050679
LabelBlue Cone Monochromacy