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Autosomal Recessive Congenital Ichthyosis 7

Disease ID: disease_node_19976

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DbxrefICD10CM:Q80.2, MIM:615022
SubclassofDOID_0060655
Data SourceDOID
SynonymsARCI7
Doid Labelautosomal recessive congenital ichthyosis 7
Doid DescriptionAn autosomal recessive congenital ichthyosis characterized by fine whitish scales, moderate to severe erythroderma, compact hyperkeratosis, hypergranulosis, acanthosis, and papillomatosis that has_material_basis_in variation in the chromosome region 12p11.2-q13.1.
Disease Node Iddisease_node_19976
Doid IdDOID_0060716
Disease Has Basis InHP_0001197
LabelAutosomal Recessive Congenital Ichthyosis 7