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Adult Onset Demyelinating Leukodystrophy

Disease ID: disease_node_19955

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DbxrefMIM:PS169500, ORDO:99027
SubclassofDOID_10579
Data SourceDOID
SynonymsAutosomal dominant leukodystrophy with autonomic disease, autosomal dominant adult-onset demyelinating leukodystrophy
Doid Labeladult onset demyelinating leukodystrophy
Doid DescriptionA leukodystrophy that is characterized by central nervous system demyelination, leading to autonomic dysfunction, ataxia and mild cognitive impairment.
Disease Node Iddisease_node_19955
Doid IdDOID_0051015
LabelAdult Onset Demyelinating Leukodystrophy