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Isolated Growth Hormone Deficiency Type Ia

Disease ID: disease_node_19698

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DbxrefICD10CM:E23.0, MIM:262400, ORDO:231662
SubclassofDOID_0060870
Data SourceDOID
SynonymsIGHD IA, Illig-type growth hormone deficiency, autosomal recessive isolated growth hormone deficiency, pituitary dwarfism I, primordial dwarfism, sexual ateleiotic dwarfism
Doid Labelisolated growth hormone deficiency type IA
Doid DescriptionAn isolated growth hormone deficiency characterized by autosomal recessive inheritance of severe dwarfism with onset by 6 months of age and variable development of antibodies to growth hormone following exogenous supplementation that has_material_basis_in null mutations in the GH1 gene on chromosome 17q23.3.
Disease Node Iddisease_node_19698
Doid IdDOID_0060873
LabelIsolated Growth Hormone Deficiency Type Ia