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Familial Episodic Pain Syndrome 1

Disease ID: disease_node_19411

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DbxrefMIM:615040, ORDO:391389
SubclassofDOID_0050736, DOID_0111728
Data SourceDOID
SynonymsFEPS1
Doid Labelfamilial episodic pain syndrome 1
Doid DescriptionA familial episodic pain syndrome characterized by onset in infancy of episodic debilitating upper body pain triggered by fasting, cold, and physical stress that has_material_basis_in heterozygous mutation in the TRPA1 gene on chromosome 8q13.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19411
Doid IdDOID_0111729
LabelFamilial Episodic Pain Syndrome 1