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Congenital Malabsorptive Diarrhea 4

Disease ID: disease_node_19333

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DbxrefICD10CM:P78.3, MIM:610370, ORDO:83620
SubclassofDOID_0050737, DOID_0060774
Data SourceDOID
Synonymscongenital malabsorptive diarrhea due to paucity of enteroendocrine cells, congenital malabsorptive diarrhoea 4, congenital malabsorptive diarrhoea due to paucity of enteroendocrine cells, enteric anendocrinosis
Doid Labelcongenital malabsorptive diarrhea 4
Doid DescriptionA congenital diarrhea characterized by chronic unremitting malabsorptive diarrhea and a profound dysgenesis of the enteroendocrine cells that has_material_basis_in mutation in the gene encoding neurogenin-3 (NEUROG3) on chromosome 10q21.3.
Has SymptomSYMP_0000570
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_19333
Doid IdDOID_0060779
Disease Has Basis InHP_0001197
LabelCongenital Malabsorptive Diarrhea 4