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Lissencephaly 1

Disease ID: disease_node_19266

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DbxrefMIM:607432, ORDO:95232
SubclassofDOID_0050736, DOID_0050453
Data SourceDOID
SynonymsLIS1, PAFAH1B1-related lissencephaly
Doid Labellissencephaly 1
Doid DescriptionA lissencephaly characterized by an abnormally thick cortex, reduced or abnormal lamination, and diffuse neuronal heterotopia that has_material_basis_in mutation heterozygous in the PAFAH1B1 gene on chromosome 17p13.3.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19266
Doid IdDOID_0112237
LabelLissencephaly 1