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Orofaciodigital Syndrome Xviii

Disease ID: disease_node_19251

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DbxrefMIM:617927, ORDO:508501
SubclassofDOID_0050737, DOID_4501
Data SourceDOID
SynonymsOral-facial-digital syndrome type 18, Oral-facial-digital syndrome with short stature and brachymesophalangy, Orofaciodigital syndrome type 18
Doid Labelorofaciodigital syndrome XVIII
Doid DescriptionAn orofaciodigital syndrome that is characterized by short stature, brachymesophalangy, pre- and postaxial polysyndactyly, and stocky femoral necks, as well as oral anomalies and dysmorphic facial features that has_material_basis_in homozygous mutation in the IFT57 gene on chromosome 3q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_19251
Doid IdDOID_0060961
LabelOrofaciodigital Syndrome Xviii