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Linear Skin Defects With Multiple Congenital Anomalies 2

Disease ID: disease_node_19244

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DbxrefMIM:300887
SubclassofDOID_0111875, DOID_0080015, DOID_0080009
Data SourceDOID
SynonymsAPLCC, LSDMCA2, aplasia cutis congenita, reticulolinear, with microcephaly, facial dysmorphism, and other congenital anomalies
Doid Labellinear skin defects with multiple congenital anomalies 2
Doid DescriptionA linear skin defects with multiple congenital anomalies characterized by linear skin defects, microcephaly, facial dysmorphism, and other congenital anomalies that has_material_basis_in heterozygous mutation in the COX7B gene on chromosome Xq21.1.
Has Material Basis InGENO_0000146
Disease Node Iddisease_node_19244
Doid IdDOID_0111877
Disease Has Basis InHP_0001197
LabelLinear Skin Defects With Multiple Congenital Anomalies 2