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X-Linked Intellectual Disability-Psychosis-Macroorchidism Syndrome

Disease ID: disease_node_19236

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DbxrefICD10CM:F71.1, MIM:300055, ORDO:3077
SubclassofDOID_0060309
Data SourceDOID
SynonymsLindsay-Burn syndrome, MRXS13, PPM-X, X-linked mental retardation 79, X-linked mental retardation with spasticity, mental retardation with psychosis, pyramidal signs, and macroorchidism, mental retardation, X-linked, syndromic 13
Doid LabelX-linked intellectual disability-psychosis-macroorchidism syndrome
Doid DescriptionA syndromic X-linked intellectual disability characterized by moderate intellectual deficit, manic-depressive psychosis, pyramidal signs and macroorchidism that has_material_basis_in mutation in the MECP2 gene on chromosome Xq28.
Disease Node Iddisease_node_19236
Doid IdDOID_0060827
LabelX-Linked Intellectual Disability-Psychosis-Macroorchidism Syndrome