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3-Methylglutaconic Aciduria With Deafness, Encephalopathy, And Leigh-Like Syndrome

Disease ID: disease_node_19198

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DbxrefMIM:614739, ORDO:352328
SubclassofDOID_0060336, DOID_0050737
Data SourceDOID
Synonyms3-methylglutaconic aciduria type 6, MEGDEL, MEGDEL syndrome, MGCA6
Doid Label3-methylglutaconic aciduria with deafness, encephalopathy, and Leigh-like syndrome
Doid DescriptionA 3-methylglutaconic aciduria that has_material_basis_in homozygous or compound heterozygous mutation in the SERAC1 gene on chromosome 6q25.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_19198
Doid IdDOID_0110001
Label3-Methylglutaconic Aciduria With Deafness, Encephalopathy, And Leigh-Like Syndrome