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3-Methylglutaconic Aciduria Type 3

Disease ID: disease_node_19194

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DbxrefMIM:258501, ORDO:67047
SubclassofDOID_0060336, DOID_0050737
Data SourceDOID
Synonyms3-methylglutaconic aciduria type III, Costeff optic atrophy syndrome, Costeff syndrome, Iraqi-Jewish optic atrophy plus, MGA3, autosomal recessive optic atrophy plus syndrome, autosomal recessive optic atrophy type 3, infantile optic atrophy with chorea and spastic paraplegia
Doid Label3-methylglutaconic aciduria type 3
Doid DescriptionA 3-methylglutaconic aciduria that has_material_basis_in mutation in the OPA3 gene.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_19194
Doid IdDOID_0110004
Label3-Methylglutaconic Aciduria Type 3