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Ocular Albinism With Sensorineural Deafness

Disease ID: disease_node_19184

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DbxrefICD10CM:E70.3, ORDO:352740
SubclassofDOID_0050736, DOID_0080578, DOID_0050633
Data SourceDOID
SynonymsWS2-OA, autosomal recessive Waardenburg syndrome type 2 with ocular albinism, digenic Waardenburg syndrome/albinism, digenic Waardenburg syndrome/ocular albinism
Doid Labelocular albinism with sensorineural deafness
Doid DescriptionAn ocular albinism that is characterized by deafness and vestibular dysfunction and has_material_basis_in digenic inheritance of a mutation in the transcription factor gene MITF on chromosome 3p13 and in the tyrosinase TYR gene on chromosome 11q14.3 that MITF regulates.
Has Material Basis InGENO_0000147, GENO_0000930
Disease Node Iddisease_node_19184
Doid IdDOID_0090100
LabelOcular Albinism With Sensorineural Deafness