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Erythrokeratodermia Variabilis Et Progressiva 3

Disease ID: disease_node_19135

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DbxrefMIM:617525
SubclassofDOID_0050736, DOID_0050467
Data SourceDOID
Doid Labelerythrokeratodermia variabilis et progressiva 3
Doid DescriptionAn erythrokeratodermia variabilis that is characterized by normal skin at birth but develop hyperpigmentation and scaling at sites of friction in childhood, with progression to near-confluent corrugated hyperkeratosis, palmoplantar keratoderma, and transient figurate erythema and that has_material_basis_in heterozygous mutation in the gene encoding connexin-43 (GJA1) on chromosome 6q22.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19135
Doid IdDOID_0080249
LabelErythrokeratodermia Variabilis Et Progressiva 3