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Contractures, Pterygia, And Spondylocarpotarsal Fusion Syndrome 1B

Disease ID: disease_node_19118

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DbxrefGARD:7111, MIM:618469, ORDO:2990
SubclassofDOID_0080110, DOID_0050737
Data SourceDOID
SynonymsAutosomal recessive multiple pterygium syndrome
Doid Labelcontractures, pterygia, and spondylocarpotarsal fusion syndrome 1B
Doid DescriptionA contractures, pterygia, and spondylocarpotarsal fusion syndrome that is characterized by contractures of proximal and distal joints, pterygia involving the neck, elbows, fingers, and/or knees, and variable vertebral, carpal, and tarsal fusions and that has_material_basis_in compound heterozygous mutation in the MYH3 gene on chromosome 17p13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_19118
Doid IdDOID_0081322
LabelContractures, Pterygia, And Spondylocarpotarsal Fusion Syndrome 1B