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Crouzon Syndrome-Acanthosis Nigricans Syndrome

Disease ID: disease_node_19032

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DbxrefMIM:612247, ORDO:93262
SubclassofDOID_0050736, DOID_225, DOID_0080001
Data SourceDOID
SynonymsCAN, Crouzon-dermoskeletal syndrome, Crouzonodermoskeletal syndrome
Disease Has LocationUBERON_0004766
Doid LabelCrouzon syndrome-acanthosis nigricans syndrome
Doid DescriptionA syndrome characterized by Crouzon-like features, premature synostosis of cranial sutures, and acanthosis nigricans that has_material_basis_in heterozygous missense mutation in the FGFR3 gene on chromosome 4p16.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19032
Doid IdDOID_0111161
LabelCrouzon Syndrome-Acanthosis Nigricans Syndrome