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Myofibrillar Myopathy 1

Disease ID: disease_node_18984

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DbxrefICD10CM:G71.0, MIM:601419, ORDO:363543
SubclassofDOID_0050736, DOID_0080307, DOID_0050737
Data SourceDOID
Synonymsautosomal recessive limb-girdle muscular dystrophy type 2R, desminopathy
Doid Labelmyofibrillar myopathy 1
Doid DescriptionA myofibrillar myopathy that has_material_basis_in heterozygous, homozygous, or compound heterozygous mutation in the desmin gene on chromosome 2q35.
Has Material Basis InGENO_0000147, GENO_0000148
Disease Node Iddisease_node_18984
Doid IdDOID_0080092
LabelMyofibrillar Myopathy 1
Doid Alternate IdsDOID_0110286