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Myofibrillar Myopathy 9

Disease ID: disease_node_18975

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DbxrefGARD:12591, MIM:603689, ORDO:178464
SubclassofDOID_0080307
Data SourceDOID
SynonymsEdstrom myopathy, HIBM-ERF, HMERF, Hereditary inclusion body myopathy with early respiratory failure, MFM-titinopathy, MFM9, MPRM, Myofibrillar myopathy-titinopathy, autosomal dominant distal myopathy with early respiratory failure, hereditary myopathy with early respiratory failure, myofibrillar myopathy 9 with early respiratory failure, proximal myopathy with early respiratory muscle involvement
Doid Labelmyofibrillar myopathy 9
Doid DescriptionA myofibrillar myopathy characterized by adult onset of slowly progressive muscle weakness involving the diaphragm and resulting in respiratory insufficiency that has_material_basis_in heterozygous mutation in the TTN gene on chromosome 2q31.
Has SymptomSYMP_0000363, SYMP_0000094
Disease Node Iddisease_node_18975
Doid IdDOID_0111188
LabelMyofibrillar Myopathy 9