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Autosomal Recessive Limb-Girdle Muscular Dystrophy Type 2D

Disease ID: disease_node_18905

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DbxrefICD10CM:G71.0, MIM:608099, ORDO:62
SubclassofDOID_0110274
Data SourceDOID
SynonymsAlpha-sarcoglycanopathy, DMDA2, Duchenne-like autosomal recessive muscular dystrophy type 2, LGMD2D, muscular dystrophy, limb-girdle, type 2D, primary adhalinopathy
Doid Labelautosomal recessive limb-girdle muscular dystrophy type 2D
Doid DescriptionAn autosomal recessive limb-girdle muscular dystrophy that has_material_basis_in homozygous or compound heterozygous mutation in the alpha-sarcoglycan gene (SGCA) on chromosome 17q.
Disease Node Iddisease_node_18905
Doid IdDOID_0110278
LabelAutosomal Recessive Limb-Girdle Muscular Dystrophy Type 2D