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Autosomal Recessive Limb-Girdle Muscular Dystrophy Type 2E

Disease ID: disease_node_18904

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DbxrefICD10CM:G71.0, MIM:604286, ORDO:119
SubclassofDOID_0110274
Data SourceDOID
SynonymsBeta-sarcoglycanopathy, LGMD2E, Limb-girdle muscular dystrophy due to beta-sarcoglycan deficiency, muscular dystrophy, limb-girdle, type 2E
Doid Labelautosomal recessive limb-girdle muscular dystrophy type 2E
Doid DescriptionAn autosomal recessive limb-girdle muscular dystrophy that has_material_basis_in homozygous or compound heterozygous mutation in the gene encoding beta-sarcoglycan (SGCB) on chromosome 4q12.
Disease Node Iddisease_node_18904
Doid IdDOID_0110279
LabelAutosomal Recessive Limb-Girdle Muscular Dystrophy Type 2E