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Autosomal Recessive Limb-Girdle Muscular Dystrophy Type 2Y

Disease ID: disease_node_18895

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DbxrefICD10CM:G71.0, MIM:617072, ORDO:424261
SubclassofDOID_0110274
Data SourceDOID
SynonymsLGMD2Y, autosomal recessive muscular dystrophy due to LAP1B deficiency, autosomal recessive muscular dystrophy due to Torsin-1A-interacting protein 1 deficiency, muscular dystrophy with progressive weakness, distal contractures and rigid spine, muscular dystrophy, limb-girdle, type 2Y
Doid Labelautosomal recessive limb-girdle muscular dystrophy type 2Y
Doid DescriptionAn autosomal recessive limb-girdle muscular dystrophy that has_material_basis_in homozygous mutation in the TOR1AIP1 gene on chromosome 1q24.
Disease Node Iddisease_node_18895
Doid IdDOID_0110289
LabelAutosomal Recessive Limb-Girdle Muscular Dystrophy Type 2Y