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Charcot-Marie-Tooth Disease Recessive Intermediate C

Disease ID: disease_node_18820

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DbxrefICD10CM:G60.0, MIM:615376, ORDO:369867
SubclassofDOID_0050543, DOID_0050737
Data SourceDOID
SynonymsCMTRIC, RI-CMT type C, RI-CMTC, autosomal recessive intermediate Charcot-Marie-Tooth disease type C
Doid LabelCharcot-Marie-Tooth disease recessive intermediate C
Doid DescriptionA Charcot-Marie-Tooth disease intermediate type that has_material_basis_in homozygous or compound heterozygous mutation in the PLEKHG5 gene on chromosome 1p36.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18820
Doid IdDOID_0110198
LabelCharcot-Marie-Tooth Disease Recessive Intermediate C