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Ehlers-Danlos Syndrome Classic-Like 2

Disease ID: disease_node_18765

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DbxrefMIM:618000
SubclassofDOID_0050737, DOID_13359
Data SourceDOID
Doid LabelEhlers-Danlos syndrome classic-like 2
Doid DescriptionAn Ehlers-Danlos syndrome that has_material_basis_in homozygous or compound heterozygous mutation in the AEBP1 gene on chromosome 7p13 and that is characterized by severe joint and skin laxity, osteoporosis involving the hips and spine, osteoarthritis, soft redundant skin that can be acrogeria-like, delayed wound healing with abnormal atrophic scarring, and shoulder, hip, knee, and ankle dislocations.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18765
Doid IdDOID_0080732
LabelEhlers-Danlos Syndrome Classic-Like 2