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Amelogenesis Imperfecta Type 2A6

Disease ID: disease_node_18115

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DbxrefMIM:617217
SubclassofDOID_0050737, DOID_2187
Data SourceDOID
SynonymsAmelogenesis imperfecta, hypomaturation type, IIA6
Doid Labelamelogenesis imperfecta type 2A6
Doid DescriptionAn amelogenesis imperfecta that is characterized by enamel of normal thickness that is hypomineralized and has a mottled appearance and that has_material_basis_in homozygous mutation in the G protein-coupled receptor-68 (GPR68) on chromosome 14q32.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18115
Doid IdDOID_0080960
LabelAmelogenesis Imperfecta Type 2A6