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Amelogenesis Imperfecta Type 1H

Disease ID: disease_node_18111

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DbxrefICD10CM:K00.5, MIM:616221
SubclassofDOID_0050737, DOID_2187
Data SourceDOID
SynonymsAI1H, amelogenesis imperfecta type IH
Doid Labelamelogenesis imperfecta type 1H
Doid DescriptionAn amelogenesis imperfecta that has_material_basis_in homozygous or compound heterozygous mutation in the integrin beta-6 gene (ITGB6) on chromosome 2q24.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18111
Doid IdDOID_0110064
LabelAmelogenesis Imperfecta Type 1H