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Amelogenesis Imperfecta Type 1G

Disease ID: disease_node_18109

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DbxrefICD10CM:K00.5, MIM:204690, ORDO:1031
SubclassofDOID_0050737, DOID_2187
Data SourceDOID
SynonymsAI1G, AIGFS, ERS, amelogenesis imperfecta and gingival fibromatosis syndrome, amelogenesis imperfecta hypoplastic with nephrocalcinosis, amelogenesis imperfecta type IG, enamel-renal syndrome, enamel-renal-gingival syndrome
Doid Labelamelogenesis imperfecta type 1G
Doid DescriptionAn amelogenesis imperfecta that has_material_basis_in homozygous or compound heterozygous mutation in the FAM20A gene on chromosome 17q24.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18109
Doid IdDOID_0110066
LabelAmelogenesis Imperfecta Type 1G