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Amelogenesis Imperfecta Type 1B

Disease ID: disease_node_18108

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DbxrefICD10CM:K00.5, MIM:104500
SubclassofDOID_0050736, DOID_2187
Data SourceDOID
SynonymsAI1B, AIH2, amelogenesis imperfecta type IB, autosomal dominant hypoplastic local amelogenesis imperfecta, hereditary localized enamel hypoplasia
Doid Labelamelogenesis imperfecta type 1B
Doid DescriptionAn amelogenesis imperfecta that has_material_basis_in heterozygous mutation in the enamelin gene (ENAM) on chromosome 4q13.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_18108
Doid IdDOID_0110052
LabelAmelogenesis Imperfecta Type 1B