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Amelogenesis Imperfecta Type 1A

Disease ID: disease_node_18106

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DbxrefICD10CM:K00.5, MIM:104530
SubclassofDOID_0050736, DOID_2187
Data SourceDOID
SynonymsAI1A, amelogenesis imperfecta hypoplastic type IA, amelogenesis imperfecta type IA
Doid Labelamelogenesis imperfecta type 1A
Doid DescriptionAn amelogenesis imperfecta that has_material_basis_in heterozygous mutation in the beta-3 laminin gene (LAMB3) on chromosome 1q32.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_18106
Doid IdDOID_0110054
LabelAmelogenesis Imperfecta Type 1A