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Amelogenesis Imperfecta Type 2A1

Disease ID: disease_node_18104

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DbxrefGARD:9495, ICD10CM:K00.5, MIM:204700
SubclassofDOID_0050737, DOID_2187
Data SourceDOID
SynonymsAI2A1, amelogenesis imperfecta pigmented hypomaturation type 1, amelogenesis imperfecta type IIA1
Doid Labelamelogenesis imperfecta type 2A1
Doid DescriptionAn amelogenesis imperfecta that has_material_basis_in homozygous mutation in the kallikrein-4 gene (KLK4) on chromosome 19q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18104
Doid IdDOID_0110057
LabelAmelogenesis Imperfecta Type 2A1