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Ectodermal Dysplasia 11B

Disease ID: disease_node_18094

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DbxrefMIM:614941
SubclassofDOID_0050737, DOID_14793
Data SourceDOID
SynonymsECTD11B, ectodermal dysplasia 11B, hypohidrotic/hair/tooth type, autosomal recessive
Doid Labelectodermal dysplasia 11B
Doid DescriptionA hypohidrotic ectodermal dysplasia that has_material_basis_in homozygous or compound heterozygous mutation in the EDARADD gene on chromosome 1q42-q43.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_18094
Doid IdDOID_0111654
LabelEctodermal Dysplasia 11B