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Ectodermal Dysplasia And Immunodeficiency 1

Disease ID: disease_node_18091

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DbxrefMIM:300291, ORDO:69088
SubclassofDOID_0080012, DOID_0081077
Data SourceDOID
Doid Labelectodermal dysplasia and immunodeficiency 1
Doid DescriptionAn ectodermal dysplasia and immunodeficiency that is characterized by onset of recurrent severe infections due to immunodeficiency in early infancy or in the first years of life and that has_material_basis_in hemizygous mutation in the IKK-gamma gene (IKBKG) on chromosome Xq28.
Has PhenotypeHP_0010978
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_18091
Doid IdDOID_0081078
LabelEctodermal Dysplasia And Immunodeficiency 1