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Spinal Muscular Atrophy With Lower Extremity Predomit 2B

Disease ID: disease_node_18026

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DbxrefMIM:618291
SubclassofDOID_0070348
Data SourceDOID
Synonymsspinal muscular atrophy with lower extremity predominance 2B
Doid Labelspinal muscular atrophy with lower extremity predomit 2B
Doid DescriptionA spinal muscular atrophy with lower extremity predomice that is characterized by decreased fetal movements and are congenital contractures consistent with arthrogryposis multiplex congenita and that has_material_basis_in heterozygous mutation in the BICD2 gene on chromosome 9q22.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_18026
Doid IdDOID_0070350
LabelSpinal Muscular Atrophy With Lower Extremity Predomit 2B