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Autosomal Domit Distal Hereditary Motor Neuronopathy

Disease ID: disease_node_18002

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DbxrefMIM:PS182960, ORDO:140465
SubclassofDOID_0050736, DOID_12377
Data SourceDOID
Synonymsautosomal dominant dHMN, autosomal dominant distal hereditary motor neuropathy, autosomal dominant distal spinal muscular atrophy
Disease Has LocationUBERON_0002257
Doid Labelautosomal domit distal hereditary motor neuronopathy
Doid DescriptionA spinal muscular atrophy that is characterized by progressive distal motor weakness and muscular atrophy of the peripheral nervous system without sensory impairment, that is caused by anterior horn cell degeneration, and that has_material_basis_in autosomal domit inheritance.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_18002
Doid IdDOID_0111198
LabelAutosomal Domit Distal Hereditary Motor Neuronopathy