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Congenital Adrenal Insufficiency

Disease ID: disease_node_17794

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DbxrefMIM:613743
SubclassofDOID_0050736, DOID_0080015, DOID_0050737, DOID_9553
Data SourceDOID
SynonymsADRENAL INSUFFICIENCY, CONGENITAL, WITH 46,XY SEX REVERSAL, PARTIAL OR COMPLETE, Adrenal insufficiency, congenital, with 46,XY sex reversal, P450scc DEFICIENCY
Doid Labelcongenital adrenal insufficiency
Doid DescriptionAn adrenal gland disease that is characterized by cortisol deficiency, hypoaldosteronism and excessive or insufficient sex hormones, has_material_basis_in the mutation in the gene for 21-hydroxylase, 11beta-hydroxylase, 3beta-hydroxysteroid, 17alpha-hydroxylase or 20,22-desmolase. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147, GENO_0000148
Disease Node Iddisease_node_17794
Doid IdDOID_0050546
Disease Has Basis InHP_0001197
LabelCongenital Adrenal Insufficiency