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Progressive Familial Intrahepatic Cholestasis 4

Disease ID: disease_node_17768

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DbxrefMIM:615878, ORDO:480483
SubclassofDOID_0070221, DOID_0050737
Data SourceDOID
SynonymsPFIC4, TJP2 deficit
Doid Labelprogressive familial intrahepatic cholestasis 4
Doid DescriptionA progressive familial intrahepatic cholestasis characterized by autosomal recessive inheritance that has_material_basis_in mutation in the TJP2 gene on chromosome 9q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17768
Doid IdDOID_0070224
LabelProgressive Familial Intrahepatic Cholestasis 4