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Peroxisome Biogenesis Disorder 1B

Disease ID: disease_node_17527

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DbxrefMIM:601539
SubclassofDOID_0080377, DOID_0050737
Data SourceDOID
Doid Labelperoxisome biogenesis disorder 1B
Doid DescriptionA peroxisome biogenesis disorder that is characterized by the overlapping phenotypes of neonatal adrenoleukodystrophy and infantile Refsum disease and that has_material_basis_in homozygous or compound heterozygous mutation in the PEX1 gene on chromosome 7q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17527
Doid IdDOID_0081240
LabelPeroxisome Biogenesis Disorder 1B