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Peroxisome Biogenesis Disorder 5B

Disease ID: disease_node_17523

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DbxrefMIM:614867
SubclassofDOID_0080377, DOID_0050737
Data SourceDOID
Doid LabelPeroxisome biogenesis disorder 5B
Doid DescriptionA peroxisomal biogenesis disorder that is characterized by the overlapping phenotypes of neonatal adrenoleukodystrophy and infantile Refsum disease and that has_material_basis_in homozygous or compound heterozygous mutation in the PEX2 gene on chromosome 8q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17523
Doid IdDOID_0081434
LabelPeroxisome Biogenesis Disorder 5B