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Peroxisome Biogenesis Disorder 7B

Disease ID: disease_node_17521

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DbxrefMIM:614873
SubclassofDOID_0080377, DOID_0050737
Data SourceDOID
Doid LabelPeroxisome biogenesis disorder 7B
Doid DescriptionA peroxisomal biogenesis disorder that is characterized by the overlapping phenotypes of neonatal adrenoleukodystrophy and infantile Refsum disease and that has_material_basis_in homozygous or compound heterozygous mutation in the PEX26 gene on chromosome 22q11.21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17521
Doid IdDOID_0081436
LabelPeroxisome Biogenesis Disorder 7B