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Peroxisome Biogenesis Disorder 9B

Disease ID: disease_node_17519

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DbxrefMIM:614879
SubclassofDOID_0080377, DOID_0050737
Data SourceDOID
Doid LabelPeroxisome biogenesis disorder 9B
Doid DescriptionA peroxisomal biogenesis disorder that is characterized by the overlapping phenotypes of neonatal adrenoleukodystrophy and infantile Refsum disease and that has_material_basis_in homozygous or compound heterozygous mutation in the PEX7 gene on chromosome 6q23.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17519
Doid IdDOID_0081438
LabelPeroxisome Biogenesis Disorder 9B