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Xanthinuria

Disease ID: disease_node_17500

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DbxrefICD10CM:E79.8, MIM:PS278300, ORDO:3467, SNOMEDCT_US_2023_03_01:190919008, UMLS_CUI:C0220988
SubclassofDOID_653, DOID_0050737
Data SourceDOID
Synonymsclassic xanthinuria, hereditary xanthinuria, xanthine dehydrogenase deficiency, xanthine oxidase deficiency
Doid Labelxanthinuria
Doid DescriptionA purine-pyrimidine metabolic disorder characterized by deficiency of xanthine oxidase, resulting in excretion of large amounts of xanthine in the urine and the formation of xanthine stones. NT MGI.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17500
Doid IdDOID_0060236
LabelXanthinuria