This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Hrpt-Related Hyperuricemia

Disease ID: disease_node_17480

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:300323, ORDO:79233
SubclassofDOID_0080012, DOID_1920, DOID_655
Data SourceDOID
SynonymsHPRT deficiency, grade I, HPRT partial deficiency, HPRT-related gout, HPRT-related hyperuricemia, HPRT1 partial deficiency, Kelley-Seegmiller syndrome, hypoxanthine guanine phosphoribosyltransferase 1 partial deficiency, hypoxanthine guanine phosphoribosyltransferase deficiency, grade I, hypoxanthine guanine phosphoribosyltransferase partial deficiency
Doid LabelHRPT-related hyperuricemia
Doid DescriptionA hyperuricemia characterized by excessive purine production often resulting in renal stones, uric acid nephropathy, and renal obstruction that has_material_basis_in hemizygous mutation in the HPRT1 gene on chromosome Xq26.2-q26.3.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_17480
Doid IdDOID_0112127
LabelHrpt-Related Hyperuricemia