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Poorly Differentiated Chordoma

Disease ID: disease_node_17433

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DbxrefICDO:9370/3, NCI:C177898
SubclassofDOID_3302
Data SourceDOID
Doid Labelpoorly differentiated chordoma
Doid DescriptionA chordoma that is characterized by loss of SMARCB1 expression and that is composed of sheets or nests of maligt epithelioid cells with abundant eosinophilic cytoplasm.
Disease Node Iddisease_node_17433
Doid IdDOID_0081417
LabelPoorly Differentiated Chordoma