This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Congenital Muscular Dystrophy Due To Integrin Alpha-7 Deficiency

Disease ID: disease_node_17429

Connections displayed (default: 10).
Loading graph...

DbxrefICD10CM:G71.2, MIM:613204, ORDO:34520
SubclassofDOID_0050737, DOID_0050557
Data SourceDOID
Synonymscongenital muscular dystrophy with ITGA7 deficiency, congenital muscular dystrophy with integrin alpha-7 deficiency, congenital myopathy due to integrin alpha-7 deficiency
Doid Labelcongenital muscular dystrophy due to integrin alpha-7 deficiency
Doid DescriptionA congenital muscular dystrophy characterized by autosomal recessive inheritance that has_material_basis_in compound heterozygous mutation in the ITGA7 gene on chromosome 12q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17429
Doid IdDOID_0110639
Disease Has Basis InHP_0001197
LabelCongenital Muscular Dystrophy Due To Integrin Alpha-7 Deficiency