This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Congenital Muscular Dystrophy-Dystroglycanopathy Type A

Disease ID: disease_node_17406

Connections displayed (default: 10).
Loading graph...

DbxrefMIM:PS236670, ORDO:352687
SubclassofDOID_0112374, DOID_0050737
Data SourceDOID
SynonymsMDDGA, congenital muscular alpha-dystroglycanopathy with brain and eye anomalies, klissencephaly type 2 with muscular and ocular involvement
Doid Labelcongenital muscular dystrophy-dystroglycanopathy type A
Doid DescriptionA congenital muscular dystrophy-dystroglycanopathy characterized by cobblestone lissencephaly, muscle weakness, and brain and eye anomalies that has_material_basis_in autosomal recessive inheritance a defect in alpha-dystroglycan post-translational processing.
Has SymptomSYMP_0000094
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17406
Doid IdDOID_0111229
Disease Has Basis InHP_0001197
LabelCongenital Muscular Dystrophy-Dystroglycanopathy Type A