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Autosomal Recessive Osteopetrosis 5

Disease ID: disease_node_17391

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DbxrefGARD:4153, MIM:259720
SubclassofDOID_13533, DOID_0050737
Data SourceDOID
SynonymsOPTB5, infantile malignant osteopetrosis 3
Doid Labelautosomal recessive osteopetrosis 5
Doid DescriptionAn osteopetrosis characterized by autosomal recessive inheritance that has_material_basis_in mutation in the OSTM1 gene on chromosome 6q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17391
Doid IdDOID_0110939
LabelAutosomal Recessive Osteopetrosis 5