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Autosomal Recessive Osteopetrosis 3

Disease ID: disease_node_17389

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DbxrefGARD:4154, MIM:259730
SubclassofDOID_13533, DOID_0050737
Data SourceDOID
SynonymsGuibaud-Vainsel syndrome, OPTB3, autosomal recessive osteopetrosis 3 with renal tubular acidosis, carbonic anhydrase II deficiency, marble brain disease, osteopetrosis with renal tubular acidosis
Doid Labelautosomal recessive osteopetrosis 3
Doid DescriptionAn osteopetrosis characterized by autosomal recessive inheritance that has_material_basis_in homozygous or compound heterozygous mutation in the CA2 gene on chromosome 8q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17389
Doid IdDOID_0110941
LabelAutosomal Recessive Osteopetrosis 3