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Autosomal Recessive Osteopetrosis 1

Disease ID: disease_node_17388

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DbxrefGARD:2579, MIM:259700
SubclassofDOID_13533, DOID_0050737
Data SourceDOID
SynonymsOPTB1, autosomal recessive Albers-Schonberg disease, infantile malignant osteopetrosis 1
Doid Labelautosomal recessive osteopetrosis 1
Doid DescriptionAn osteopetrosis characterized by autosomal recessive inheritance that has_material_basis_in homozygous or compound heterozygous mutation in the TCIRG1 gene on chromosome 11q13.2.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17388
Doid IdDOID_0110942
LabelAutosomal Recessive Osteopetrosis 1