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Autosomal Recessive Osteopetrosis 6

Disease ID: disease_node_17385

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DbxrefGARD:4156, MIM:611497
SubclassofDOID_13533, DOID_0050737
Data SourceDOID
SynonymsOPTB6, autosomal recessive osteopetrosis intermediate form
Doid Labelautosomal recessive osteopetrosis 6
Doid DescriptionAn osteopetrosis characterized by autosomal recessive inheritance of that has_material_basis_in mutation in the PLEKHM1 gene on chromosome 17q21.31.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_17385
Doid IdDOID_0110945
LabelAutosomal Recessive Osteopetrosis 6