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Cinca Syndrome

Disease ID: disease_node_17360

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DbxrefICD10CM:E85.0, MIM:607115, ORDO:1451
SubclassofDOID_0050736, DOID_417
Data SourceDOID
SynonymsIOMID syndrome, NOMID syndrome, Prieur-Griscelli syndrome, chronic infantile neurological cutaneous articular syndrome, chronic neurologic cutaneous and articular syndrome, cryopyrin-associated periodic syndrome 3, infantile-onset multisystem inflammatory disease, neonatal-onset multisystem inflammatory disease
Doid LabelCINCA Syndrome
Doid DescriptionAn autoimmune disease characterized by neonatal onset of cutaneous symptoms, chronic meningitis, and joint manifestations with recurrent fever and inflammation that has_material_basis_in heterozygous mutation in the NLRP3 gene on chromosome 1q.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_17360
Doid IdDOID_0090029
LabelCinca Syndrome