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Agammaglobulinemia 10

Disease ID: disease_node_17352

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DbxrefMIM:619707
SubclassofDOID_0050736, DOID_2583
Data SourceDOID
Doid Labelagammaglobulinemia 10
Doid DescriptionAn agammaglobulinemia that is characterized by early-childhood onset of recurrent viral and bacterial infections affecting various organ systems, particularly the sinopulmonary system. and that has_material_basis_in heterozygous mutation in the SPI1 gene on chromosome 11p11.
Existence Starts DuringHP_0011463
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_17352
Doid IdDOID_0081142
LabelAgammaglobulinemia 10